Nitin Shah has done his under graduation and postgraduation from Seth. G.S.M.C and K.E.M. Hospital. Atpresent, he is working as consultant gynaec laparoscopicsurgeon. He is the director of Vardann multispecialityhospital, Poisar, Kandivali west, Mumbai. He isscientific secretary of A.F.G. and managing committeemember of I.A.G.E. He is the holder of 10 world recordsfor his laparoscopic surgeries. He is recipient of goldenhand award. He has published highest number of coverpage laparoscopic photograph articles in J.O.G.I. He has morethan 50 publications both national and international to hiscredit. He has won various awards and prizes at manynational and international conferences.
OHVIRA SYNDROME (obstructed hemivagina with ipsilateral renal agenesis) or Herlyn–Werner–Wunderlich syndrome is a very rare type of mullerian anomaly.
Twenty-six-year-old female, nulligravida, complained of pain in right iliac fossa on and off since two to three months with excessive mucoid vaginal discharge since then. She had history of regular menstrual cycles. MRI findings were suggestive of uterus didelphys with obstructed right hemivagina and the absence of right kidney and ureter as shown in Figs. 1, 2 and 3. On per speculum examination, excessive mucopurulent discharge was present. Cervix was seen on left side. Bogginess was palpable in right fornix. On per vaginal examination, broad fundus was palpable which was suggestive of congenital mullerian anomaly (uterus didelphys). Excessive mucopurulent discharge was noted.
On Hystero–laparoscopy—a cervical opening was seen on left side. A 3 cm × 3 cm bulge was seen in right fornix which was suggestive of obstructed right hemivagina. The obstruction was relieved by draining the obstructed hemivagina with the help of resectoscope. Excessive mucopurulent discharge was seen draining from the right hemivagina as shown in Figs. 4 and 5. Findings were confirmed with laparoscopy. Uterus didelphys was noted with two separate cervices with two hemi vagina( with obstructed hemivagina). Right kidney and right ureter were absent as shown in Figs 6 and 7a, b.
Authors Contribution NS: has operated this case, searched literature and done final proof reading of this article; PC: who has done fellowship in laparoscopy under NS has assisted this case, written this article, done literature search and helped in proof reading this article; VB: has assisted this case, searched literature and done proof reading of this article; SB: has assisted this case, searched literature and done proof reading of this article.
Conflict of interest The authors declare that they have no conflict of interest,
Informed Consent Informed consent taken from patient.
